{"id":550383,"date":"2026-03-05T21:58:17","date_gmt":"2026-03-05T20:58:17","guid":{"rendered":"https:\/\/medizinonline.com\/?p=550383"},"modified":"2026-03-05T21:58:27","modified_gmt":"2026-03-05T20:58:27","slug":"friedreichs-ataxia-when-the-energy-metabolism-attacks-the-nervous-system","status":"publish","type":"post","link":"https:\/\/medizinonline.com\/en\/friedreichs-ataxia-when-the-energy-metabolism-attacks-the-nervous-system\/","title":{"rendered":"Friedreich&#8217;s ataxia: when the energy metabolism attacks the nervous system"},"content":{"rendered":"\n<p><strong>Energy deficiency instead of pure oxidative stress: New data show that in Friedreich&#8217;s ataxia, disturbances in fatty acid and ketone body metabolism in particular contribute to selective neurodegeneration. The article explains the pathophysiology, explains the neuronal vulnerability and shows which metabolic signaling pathways could be addressed therapeutically in the future. <\/strong><\/p>\n\n<div class=\"pmpro\"><div class=\"pmpro_card pmpro_content_message\"><div class=\"pmpro_card_content\">Dieser Inhalt ist nur f\u00fcr Benutzer der Gruppe: Medizinische Fachperson zug\u00e4nglich <br \/><a href=\"https:\/\/medizinonline.com\/en\/my-account\/packages\/\">Jetzt beitreten<\/a><\/div><div class=\"pmpro_card_actions pmpro_font-medium\">Already a member? <a href=\"https:\/\/medizinonline.com\/en\/log-in\/?redirect_to=https%3A%2F%2Fmedizinonline.com%2Fen%2Ffriedreichs-ataxia-when-the-energy-metabolism-attacks-the-nervous-system%2F\">Log in here<\/a><\/div><\/div><\/div>","protected":false},"excerpt":{"rendered":"<p>Energy deficiency instead of pure oxidative stress: New data show that in Friedreich&#8217;s ataxia, disturbances in fatty acid and ketone body metabolism in particular contribute to selective neurodegeneration. The article&#8230;&hellip;... <\/p>\n<div class=\"pmpro\"><div class=\"pmpro_card pmpro_content_message\"><div class=\"pmpro_card_content\">Dieser Inhalt ist nur f\u00fcr Benutzer der Gruppe: Medizinische Fachperson zug\u00e4nglich <br \/><a href=\"https:\/\/medizinonline.com\/en\/my-account\/packages\/\">Jetzt beitreten<\/a><\/div><div class=\"pmpro_card_actions pmpro_font-medium\">Already a member? <a href=\"https:\/\/medizinonline.com\/en\/log-in\/?redirect_to=https%3A%2F%2Fmedizinonline.com%2Fen%2Ffriedreichs-ataxia-when-the-energy-metabolism-attacks-the-nervous-system%2F\">Log in here<\/a><\/div><\/div><\/div>","protected":false},"author":7,"featured_media":550384,"comment_status":"closed","ping_status":"closed","sticky":false,"template":"","format":"standard","meta":{"_acf_changed":false,"pmpro_default_level":"","cat_1_feature_home_top":false,"cat_2_editor_pick":false,"csco_eyebrow_text":"Ataxias","footnotes":""},"category":[11508,11396,11363,11548,11503],"tags":[88881,88882,88607,84961,88880,88879],"powerkit_post_featured":[],"class_list":["post-550383","post","type-post","status-publish","format-standard","has-post-thumbnail","category-education","category-genetics","category-neurology","category-rx-en","category-studies","tag-ataxias","tag-frataxin-deficiency","tag-frda","tag-friedreichs-ataxia","tag-friedreichs-ataxia-pathophysiology","tag-fxn","pmpro-level-required","pmpro-level-1","pmpro-no-access"],"acf":[],"publishpress_future_action":{"enabled":false,"date":"2026-04-27 01:22:14","action":"change-status","newStatus":"draft","terms":[],"taxonomy":"category","extraData":[]},"publishpress_future_workflow_manual_trigger":{"enabledWorkflows":[]},"wpml_current_locale":"en_US","wpml_translations":{"fr_FR":{"locale":"fr_FR","id":550380,"slug":"lataxie-de-friedreich-quand-le-metabolisme-energetique-sattaque-au-systeme-nerveux","post_title":"L'ataxie de Friedreich : quand le m\u00e9tabolisme \u00e9nerg\u00e9tique s'attaque au syst\u00e8me nerveux","href":"https:\/\/medizinonline.com\/fr\/lataxie-de-friedreich-quand-le-metabolisme-energetique-sattaque-au-systeme-nerveux\/"},"it_IT":{"locale":"it_IT","id":550377,"slug":"atassia-di-friedreich-quando-il-metabolismo-energetico-attacca-il-sistema-nervoso","post_title":"Atassia di Friedreich: quando il metabolismo energetico attacca il sistema nervoso","href":"https:\/\/medizinonline.com\/it\/atassia-di-friedreich-quando-il-metabolismo-energetico-attacca-il-sistema-nervoso\/"},"pt_PT":{"locale":"pt_PT","id":550374,"slug":"ataxia-de-friedreich-quando-o-metabolismo-energetico-ataca-o-sistema-nervoso","post_title":"Ataxia de Friedreich: quando o metabolismo energ\u00e9tico ataca o sistema nervoso","href":"https:\/\/medizinonline.com\/pt-pt\/ataxia-de-friedreich-quando-o-metabolismo-energetico-ataca-o-sistema-nervoso\/"},"es_ES":{"locale":"es_ES","id":550371,"slug":"ataxia-de-friedreich-cuando-el-metabolismo-energetico-ataca-al-sistema-nervioso","post_title":"Ataxia de Friedreich: cuando el metabolismo energ\u00e9tico ataca al sistema nervioso","href":"https:\/\/medizinonline.com\/es\/ataxia-de-friedreich-cuando-el-metabolismo-energetico-ataca-al-sistema-nervioso\/"}},"_links":{"self":[{"href":"https:\/\/medizinonline.com\/en\/wp-json\/wp\/v2\/posts\/550383","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/medizinonline.com\/en\/wp-json\/wp\/v2\/posts"}],"about":[{"href":"https:\/\/medizinonline.com\/en\/wp-json\/wp\/v2\/types\/post"}],"author":[{"embeddable":true,"href":"https:\/\/medizinonline.com\/en\/wp-json\/wp\/v2\/users\/7"}],"replies":[{"embeddable":true,"href":"https:\/\/medizinonline.com\/en\/wp-json\/wp\/v2\/comments?post=550383"}],"version-history":[{"count":1,"href":"https:\/\/medizinonline.com\/en\/wp-json\/wp\/v2\/posts\/550383\/revisions"}],"predecessor-version":[{"id":550385,"href":"https:\/\/medizinonline.com\/en\/wp-json\/wp\/v2\/posts\/550383\/revisions\/550385"}],"wp:featuredmedia":[{"embeddable":true,"href":"https:\/\/medizinonline.com\/en\/wp-json\/wp\/v2\/media\/550384"}],"wp:attachment":[{"href":"https:\/\/medizinonline.com\/en\/wp-json\/wp\/v2\/media?parent=550383"}],"wp:term":[{"taxonomy":"category","embeddable":true,"href":"https:\/\/medizinonline.com\/en\/wp-json\/wp\/v2\/category?post=550383"},{"taxonomy":"post_tag","embeddable":true,"href":"https:\/\/medizinonline.com\/en\/wp-json\/wp\/v2\/tags?post=550383"},{"taxonomy":"powerkit_post_featured","embeddable":true,"href":"https:\/\/medizinonline.com\/en\/wp-json\/wp\/v2\/powerkit_post_featured?post=550383"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}