{"id":397332,"date":"2025-04-07T14:00:00","date_gmt":"2025-04-07T12:00:00","guid":{"rendered":"https:\/\/medizinonline.com\/?p=397332"},"modified":"2025-04-07T14:22:41","modified_gmt":"2025-04-07T12:22:41","slug":"enfermedad-hereditaria-del-tejido-conjuntivo-con-componente-vascular","status":"publish","type":"post","link":"https:\/\/medizinonline.com\/es\/enfermedad-hereditaria-del-tejido-conjuntivo-con-componente-vascular\/","title":{"rendered":"Enfermedad hereditaria del tejido conjuntivo con componente vascular"},"content":{"rendered":"\n<p><strong>Aunque en la actualidad se dispone de pruebas gen\u00e9ticas espec\u00edficas, el diagn\u00f3stico del s\u00edndrome de Marfan sigue bas\u00e1ndose principalmente en criterios cl\u00ednicos espec\u00edficos, en particular la clasificaci\u00f3n revisada de Gante. El amplio continuo fenot\u00edpico abarca desde las manifestaciones leves hasta la enfermedad multiorg\u00e1nica neonatal grave y r\u00e1pidamente progresiva. El diagn\u00f3stico oportuno es de crucial importancia para proporcionar a los afectados las medidas de tratamiento adecuadas. Para ello se aboga por un enfoque multidisciplinar.   <\/strong><\/p>\n\n<div class=\"pmpro\"><div class=\"pmpro_card pmpro_content_message\"><div class=\"pmpro_card_content\">Dieser Inhalt ist nur f\u00fcr Benutzer der Gruppe: Medizinische Fachperson zug\u00e4nglich <br \/><a href=\"https:\/\/medizinonline.com\/es\/mi-cuenta\/paquetes\/\">Jetzt beitreten<\/a><\/div><div class=\"pmpro_card_actions pmpro_font-medium\">\u00bfYa eres miembro? <a href=\"https:\/\/medizinonline.com\/es\/conectarse\/?redirect_to=https%3A%2F%2Fmedizinonline.com%2Fes%2Fenfermedad-hereditaria-del-tejido-conjuntivo-con-componente-vascular%2F\">Accede aqu\u00ed<\/a><\/div><\/div><\/div>","protected":false},"excerpt":{"rendered":"<p>Aunque en la actualidad se dispone de pruebas gen\u00e9ticas espec\u00edficas, el diagn\u00f3stico del s\u00edndrome de Marfan sigue bas\u00e1ndose principalmente en criterios cl\u00ednicos espec\u00edficos, en particular la clasificaci\u00f3n revisada de Gante&#8230;.&hellip;... <\/p>\n<div class=\"pmpro\"><div class=\"pmpro_card pmpro_content_message\"><div class=\"pmpro_card_content\">Dieser Inhalt ist nur f\u00fcr Benutzer der Gruppe: Medizinische Fachperson zug\u00e4nglich <br \/><a href=\"https:\/\/medizinonline.com\/es\/mi-cuenta\/paquetes\/\">Jetzt beitreten<\/a><\/div><div class=\"pmpro_card_actions pmpro_font-medium\">\u00bfYa eres miembro? <a href=\"https:\/\/medizinonline.com\/es\/conectarse\/?redirect_to=https%3A%2F%2Fmedizinonline.com%2Fes%2Fenfermedad-hereditaria-del-tejido-conjuntivo-con-componente-vascular%2F\">Accede aqu\u00ed<\/a><\/div><\/div><\/div>","protected":false},"author":7,"featured_media":397333,"comment_status":"closed","ping_status":"closed","sticky":false,"template":"","format":"standard","meta":{"_acf_changed":false,"pmpro_default_level":"","cat_1_feature_home_top":false,"cat_2_editor_pick":false,"csco_eyebrow_text":"Enfermedades raras: S\u00edndrome de Marfan","footnotes":""},"category":[11324,11310,11475,11478,11288,11424,11386,11398,11402,11552],"tags":[82008,82009,26292,19421],"powerkit_post_featured":[],"class_list":["post-397332","post","type-post","status-publish","format-standard","has-post-thumbnail","category-cardiologia","category-dermatologia-y-venereologia","category-estudios","category-formacion-continua","category-medicina-interna-general","category-neumologia","category-oftalmologia","category-ortopedia","category-pediatria","category-rx-es","tag-ectopia-lentis-es","tag-enfermedad-hereditaria-del-tejido-conectivo","tag-enfermedades-raras-es","tag-sindrome-de-marfan-es","pmpro-level-required","pmpro-level-1","pmpro-no-access"],"acf":[],"publishpress_future_action":{"enabled":false,"date":"2026-05-01 01:23:42","action":"change-status","newStatus":"draft","terms":[],"taxonomy":"category","extraData":[]},"publishpress_future_workflow_manual_trigger":{"enabledWorkflows":[]},"wpml_current_locale":"es_ES","wpml_translations":[],"_links":{"self":[{"href":"https:\/\/medizinonline.com\/es\/wp-json\/wp\/v2\/posts\/397332","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/medizinonline.com\/es\/wp-json\/wp\/v2\/posts"}],"about":[{"href":"https:\/\/medizinonline.com\/es\/wp-json\/wp\/v2\/types\/post"}],"author":[{"embeddable":true,"href":"https:\/\/medizinonline.com\/es\/wp-json\/wp\/v2\/users\/7"}],"replies":[{"embeddable":true,"href":"https:\/\/medizinonline.com\/es\/wp-json\/wp\/v2\/comments?post=397332"}],"version-history":[{"count":1,"href":"https:\/\/medizinonline.com\/es\/wp-json\/wp\/v2\/posts\/397332\/revisions"}],"predecessor-version":[{"id":397335,"href":"https:\/\/medizinonline.com\/es\/wp-json\/wp\/v2\/posts\/397332\/revisions\/397335"}],"wp:featuredmedia":[{"embeddable":true,"href":"https:\/\/medizinonline.com\/es\/wp-json\/wp\/v2\/media\/397333"}],"wp:attachment":[{"href":"https:\/\/medizinonline.com\/es\/wp-json\/wp\/v2\/media?parent=397332"}],"wp:term":[{"taxonomy":"category","embeddable":true,"href":"https:\/\/medizinonline.com\/es\/wp-json\/wp\/v2\/category?post=397332"},{"taxonomy":"post_tag","embeddable":true,"href":"https:\/\/medizinonline.com\/es\/wp-json\/wp\/v2\/tags?post=397332"},{"taxonomy":"powerkit_post_featured","embeddable":true,"href":"https:\/\/medizinonline.com\/es\/wp-json\/wp\/v2\/powerkit_post_featured?post=397332"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}