{"id":563766,"date":"2026-09-07T00:30:00","date_gmt":"2026-09-06T22:30:00","guid":{"rendered":"https:\/\/medizinonline.com\/?p=563766"},"modified":"2026-09-07T07:48:12","modified_gmt":"2026-09-07T05:48:12","slug":"enfermedad-de-darier-tambien-conocida-como-queratosis-folicular-actualizacion-de-2026","status":"publish","type":"post","link":"https:\/\/medizinonline.com\/es\/enfermedad-de-darier-tambien-conocida-como-queratosis-folicular-actualizacion-de-2026\/","title":{"rendered":"Enfermedad de Darier, tambi\u00e9n conocida como queratosis folicular \u2013 Actualizaci\u00f3n de 2026"},"content":{"rendered":"\n<p class=\"wp-block-paragraph\"><strong>La enfermedad de Darier est\u00e1 causada por variantes pat\u00f3genas en el gen ATP2A2. Los avances en la comprensi\u00f3n de la fisiopatolog\u00eda han allanado el camino para el desarrollo de enfoques terap\u00e9uticos innovadores, pero es necesario seguir investigando para optimizar los resultados de los pacientes. Esto tambi\u00e9n se refleja en la creaci\u00f3n, en 2025, del <em>Grupo de Trabajo Internacional sobre la enfermedad de Darier<\/em> (DD-ITF). En pacientes con enfermedades graves o refractarias, los retinoides orales siguen consider\u00e1ndose el tratamiento sist\u00e9mico de primera l\u00ednea, pero cada vez son m\u00e1s los casos cl\u00ednicos que describen el uso satisfactorio de terapias inmunomoduladoras antiinflamatorias (inhibidores de JAK, biol\u00f3gicos). Esto apunta a que en la patog\u00e9nesis intervienen procesos inflamatorios complejos.<\/strong><\/p>\n\n<div class=\"pmpro\"><div class=\"pmpro_card pmpro_content_message\"><div class=\"pmpro_card_content\">Dieser Inhalt ist nur f\u00fcr Benutzer der Gruppe: Medizinische Fachperson zug\u00e4nglich <br \/><a href=\"https:\/\/medizinonline.com\/es\/mi-cuenta\/paquetes\/\">Jetzt beitreten<\/a><\/div><div class=\"pmpro_card_actions pmpro_font-medium\">\u00bfYa eres miembro? <a href=\"https:\/\/medizinonline.com\/es\/conectarse\/?redirect_to=https%3A%2F%2Fmedizinonline.com%2Fes%2Fenfermedad-de-darier-tambien-conocida-como-queratosis-folicular-actualizacion-de-2026%2F\">Accede aqu\u00ed<\/a><\/div><\/div><\/div>","protected":false},"excerpt":{"rendered":"<p>La enfermedad de Darier est\u00e1 causada por variantes pat\u00f3genas en el gen ATP2A2. Los avances en la comprensi\u00f3n de la fisiopatolog\u00eda han allanado el camino para el desarrollo de enfoques&#8230;&hellip;... <\/p>\n<div class=\"pmpro\"><div class=\"pmpro_card pmpro_content_message\"><div class=\"pmpro_card_content\">Dieser Inhalt ist nur f\u00fcr Benutzer der Gruppe: Medizinische Fachperson zug\u00e4nglich <br \/><a href=\"https:\/\/medizinonline.com\/es\/mi-cuenta\/paquetes\/\">Jetzt beitreten<\/a><\/div><div class=\"pmpro_card_actions pmpro_font-medium\">\u00bfYa eres miembro? <a href=\"https:\/\/medizinonline.com\/es\/conectarse\/?redirect_to=https%3A%2F%2Fmedizinonline.com%2Fes%2Fenfermedad-de-darier-tambien-conocida-como-queratosis-folicular-actualizacion-de-2026%2F\">Accede aqu\u00ed<\/a><\/div><\/div><\/div>","protected":false},"author":7,"featured_media":563767,"comment_status":"closed","ping_status":"closed","sticky":false,"template":"","format":"standard","meta":{"_acf_changed":false,"pmpro_default_level":"","cat_1_feature_home_top":false,"cat_2_editor_pick":false,"csco_eyebrow_text":"Genodermatosis raras: del diagn\u00f3stico al tratamiento","footnotes":"","_members_access_role":[],"_members_access_error":""},"category":[22619,11493,11310,11475,11408,11552],"tags":[12425,99964,14175,99959,99957,29509,99961,65872,41263,31442,99956,78225,69709],"powerkit_post_featured":[],"class_list":["post-563766","post","type-post","status-publish","format-standard","has-post-thumbnail","category-formacion-cme","category-casos","category-dermatologia-y-venereologia","category-estudios","category-farmacologia-y-toxicologia","category-rx-es","tag-biologicos-es","tag-dd-itf","tag-diagnostico-es-2","tag-enfoques-terapeuticos-innovadores","tag-gen-atp2a2","tag-genodermatosis","tag-grupo-de-trabajo-internacional-sobre-la-enfermedad-de-darier","tag-jak-i-es","tag-morbus-darier-es","tag-patogenesis","tag-queratosis-folicular","tag-retinoides-orales","tag-terapias-inmunomoduladoras","pmpro-level-required","pmpro-level-1","pmpro-no-access"],"acf":[],"publishpress_future_action":{"enabled":false,"date":"2026-09-14 09:32:33","action":"change-status","newStatus":"draft","terms":[],"taxonomy":"category","extraData":[]},"publishpress_future_workflow_manual_trigger":{"enabledWorkflows":[]},"wpml_current_locale":"es_ES","wpml_translations":[],"_links":{"self":[{"href":"https:\/\/medizinonline.com\/es\/wp-json\/wp\/v2\/posts\/563766","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/medizinonline.com\/es\/wp-json\/wp\/v2\/posts"}],"about":[{"href":"https:\/\/medizinonline.com\/es\/wp-json\/wp\/v2\/types\/post"}],"author":[{"embeddable":true,"href":"https:\/\/medizinonline.com\/es\/wp-json\/wp\/v2\/users\/7"}],"replies":[{"embeddable":true,"href":"https:\/\/medizinonline.com\/es\/wp-json\/wp\/v2\/comments?post=563766"}],"version-history":[{"count":1,"href":"https:\/\/medizinonline.com\/es\/wp-json\/wp\/v2\/posts\/563766\/revisions"}],"predecessor-version":[{"id":563770,"href":"https:\/\/medizinonline.com\/es\/wp-json\/wp\/v2\/posts\/563766\/revisions\/563770"}],"wp:featuredmedia":[{"embeddable":true,"href":"https:\/\/medizinonline.com\/es\/wp-json\/wp\/v2\/media\/563767"}],"wp:attachment":[{"href":"https:\/\/medizinonline.com\/es\/wp-json\/wp\/v2\/media?parent=563766"}],"wp:term":[{"taxonomy":"category","embeddable":true,"href":"https:\/\/medizinonline.com\/es\/wp-json\/wp\/v2\/category?post=563766"},{"taxonomy":"post_tag","embeddable":true,"href":"https:\/\/medizinonline.com\/es\/wp-json\/wp\/v2\/tags?post=563766"},{"taxonomy":"powerkit_post_featured","embeddable":true,"href":"https:\/\/medizinonline.com\/es\/wp-json\/wp\/v2\/powerkit_post_featured?post=563766"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}