{"id":397349,"date":"2025-04-07T14:00:00","date_gmt":"2025-04-07T12:00:00","guid":{"rendered":"https:\/\/medizinonline.com\/?p=397349"},"modified":"2025-04-07T14:22:39","modified_gmt":"2025-04-07T12:22:39","slug":"maladie-hereditaire-du-tissu-conjonctif-avec-composante-vasculaire","status":"publish","type":"post","link":"https:\/\/medizinonline.com\/fr\/maladie-hereditaire-du-tissu-conjonctif-avec-composante-vasculaire\/","title":{"rendered":"Maladie h\u00e9r\u00e9ditaire du tissu conjonctif avec composante vasculaire"},"content":{"rendered":"\n<p><strong>Bien qu&#8217;il existe aujourd&#8217;hui des tests g\u00e9n\u00e9tiques cibl\u00e9s, le diagnostic du syndrome de Marfan reste principalement bas\u00e9 sur des crit\u00e8res cliniques sp\u00e9cifiques, notamment la classification de Ghent r\u00e9vis\u00e9e. Le large continuum ph\u00e9notypique va de manifestations l\u00e9g\u00e8res \u00e0 des maladies n\u00e9onatales multiorganes graves et rapidement \u00e9volutives. Un diagnostic pr\u00e9coce est essentiel pour orienter les personnes concern\u00e9es vers des mesures de traitement ad\u00e9quates. Pour ce faire, une approche multidisciplinaire est pr\u00e9conis\u00e9e.   <\/strong><\/p>\n\n<div class=\"pmpro\"><div class=\"pmpro_card pmpro_content_message\"><div class=\"pmpro_card_content\">Dieser Inhalt ist nur f\u00fcr Benutzer der Gruppe: Medizinische Fachperson zug\u00e4nglich <br \/><a href=\"https:\/\/medizinonline.com\/fr\/mon-compte\/paquets\/\">Jetzt beitreten<\/a><\/div><div class=\"pmpro_card_actions pmpro_font-medium\">Already a member? <a href=\"https:\/\/medizinonline.com\/fr\/se-connecter\/?redirect_to=https%3A%2F%2Fmedizinonline.com%2Ffr%2Fmaladie-hereditaire-du-tissu-conjonctif-avec-composante-vasculaire%2F\">Connectez-vous ici<\/a><\/div><\/div><\/div>","protected":false},"excerpt":{"rendered":"<p>Bien qu&#8217;il existe aujourd&#8217;hui des tests g\u00e9n\u00e9tiques cibl\u00e9s, le diagnostic du syndrome de Marfan reste principalement bas\u00e9 sur des crit\u00e8res cliniques sp\u00e9cifiques, notamment la classification de Ghent r\u00e9vis\u00e9e. Le large&#8230;&hellip;... <\/p>\n<div class=\"pmpro\"><div class=\"pmpro_card pmpro_content_message\"><div class=\"pmpro_card_content\">Dieser Inhalt ist nur f\u00fcr Benutzer der Gruppe: Medizinische Fachperson zug\u00e4nglich <br \/><a href=\"https:\/\/medizinonline.com\/fr\/mon-compte\/paquets\/\">Jetzt beitreten<\/a><\/div><div class=\"pmpro_card_actions pmpro_font-medium\">Already a member? <a href=\"https:\/\/medizinonline.com\/fr\/se-connecter\/?redirect_to=https%3A%2F%2Fmedizinonline.com%2Ffr%2Fmaladie-hereditaire-du-tissu-conjonctif-avec-composante-vasculaire%2F\">Connectez-vous ici<\/a><\/div><\/div><\/div>","protected":false},"author":7,"featured_media":397352,"comment_status":"closed","ping_status":"closed","sticky":false,"template":"","format":"standard","meta":{"_acf_changed":false,"pmpro_default_level":"","cat_1_feature_home_top":false,"cat_2_editor_pick":false,"csco_eyebrow_text":"Maladies rares : Syndrome de Marfan","footnotes":""},"category":[11378,11362,11527,11531,11315,11444,11454,11458,11477,11549],"tags":[82018,82019,26295,19356],"powerkit_post_featured":[],"class_list":["post-397349","post","type-post","status-publish","format-standard","has-post-thumbnail","category-cardiologie","category-dermatologie-et-venerologie","category-etudes","category-formation-continue","category-medecine-interne-generale","category-ophtalmologie","category-orthopedie","category-pediatrie","category-pneumologie-fr","category-rx-fr","tag-ectopia-lentis-fr","tag-maladie-hereditaire-du-tissu-conjonctif","tag-maladies-rares-fr","tag-syndrome-de-marfan","pmpro-level-required","pmpro-level-1","pmpro-no-access"],"acf":[],"publishpress_future_action":{"enabled":false,"date":"2026-04-26 01:35:58","action":"change-status","newStatus":"draft","terms":[],"taxonomy":"category","extraData":[]},"publishpress_future_workflow_manual_trigger":{"enabledWorkflows":[]},"wpml_current_locale":"fr_FR","wpml_translations":{"it_IT":{"locale":"it_IT","id":397343,"slug":"malattia-ereditaria-del-tessuto-connettivo-con-una-componente-vascolare","post_title":"Malattia ereditaria del tessuto connettivo con una componente vascolare","href":"https:\/\/medizinonline.com\/it\/malattia-ereditaria-del-tessuto-connettivo-con-una-componente-vascolare\/"},"pt_PT":{"locale":"pt_PT","id":397337,"slug":"doenca-hereditaria-do-tecido-conjuntivo-com-um-componente-vascular","post_title":"Doen\u00e7a heredit\u00e1ria do tecido conjuntivo com um componente vascular","href":"https:\/\/medizinonline.com\/pt-pt\/doenca-hereditaria-do-tecido-conjuntivo-com-um-componente-vascular\/"},"es_ES":{"locale":"es_ES","id":397332,"slug":"enfermedad-hereditaria-del-tejido-conjuntivo-con-componente-vascular","post_title":"Enfermedad hereditaria del tejido conjuntivo con componente vascular","href":"https:\/\/medizinonline.com\/es\/enfermedad-hereditaria-del-tejido-conjuntivo-con-componente-vascular\/"}},"_links":{"self":[{"href":"https:\/\/medizinonline.com\/fr\/wp-json\/wp\/v2\/posts\/397349","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/medizinonline.com\/fr\/wp-json\/wp\/v2\/posts"}],"about":[{"href":"https:\/\/medizinonline.com\/fr\/wp-json\/wp\/v2\/types\/post"}],"author":[{"embeddable":true,"href":"https:\/\/medizinonline.com\/fr\/wp-json\/wp\/v2\/users\/7"}],"replies":[{"embeddable":true,"href":"https:\/\/medizinonline.com\/fr\/wp-json\/wp\/v2\/comments?post=397349"}],"version-history":[{"count":1,"href":"https:\/\/medizinonline.com\/fr\/wp-json\/wp\/v2\/posts\/397349\/revisions"}],"predecessor-version":[{"id":397354,"href":"https:\/\/medizinonline.com\/fr\/wp-json\/wp\/v2\/posts\/397349\/revisions\/397354"}],"wp:featuredmedia":[{"embeddable":true,"href":"https:\/\/medizinonline.com\/fr\/wp-json\/wp\/v2\/media\/397352"}],"wp:attachment":[{"href":"https:\/\/medizinonline.com\/fr\/wp-json\/wp\/v2\/media?parent=397349"}],"wp:term":[{"taxonomy":"category","embeddable":true,"href":"https:\/\/medizinonline.com\/fr\/wp-json\/wp\/v2\/category?post=397349"},{"taxonomy":"post_tag","embeddable":true,"href":"https:\/\/medizinonline.com\/fr\/wp-json\/wp\/v2\/tags?post=397349"},{"taxonomy":"powerkit_post_featured","embeddable":true,"href":"https:\/\/medizinonline.com\/fr\/wp-json\/wp\/v2\/powerkit_post_featured?post=397349"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}