{"id":550380,"date":"2026-03-05T21:58:17","date_gmt":"2026-03-05T20:58:17","guid":{"rendered":"https:\/\/medizinonline.com\/?p=550380"},"modified":"2026-03-05T21:58:29","modified_gmt":"2026-03-05T20:58:29","slug":"lataxie-de-friedreich-quand-le-metabolisme-energetique-sattaque-au-systeme-nerveux","status":"publish","type":"post","link":"https:\/\/medizinonline.com\/fr\/lataxie-de-friedreich-quand-le-metabolisme-energetique-sattaque-au-systeme-nerveux\/","title":{"rendered":"L&#8217;ataxie de Friedreich : quand le m\u00e9tabolisme \u00e9nerg\u00e9tique s&#8217;attaque au syst\u00e8me nerveux"},"content":{"rendered":"\n<p><strong>Un manque d&#8217;\u00e9nergie plut\u00f4t qu&#8217;un stress oxydatif pur : de nouvelles donn\u00e9es montrent que dans l&#8217;ataxie de Friedreich, ce sont surtout des troubles du m\u00e9tabolisme des acides gras et des corps c\u00e9toniques qui contribuent \u00e0 la neurod\u00e9g\u00e9n\u00e9rescence s\u00e9lective. L&#8217;article explique la physiopathologie, explique la vuln\u00e9rabilit\u00e9 neuronale et montre quelles voies de signalisation m\u00e9tabolique pourraient \u00eatre adress\u00e9es \u00e0 l&#8217;avenir sur le plan th\u00e9rapeutique. <\/strong><\/p>\n\n<div class=\"pmpro\"><div class=\"pmpro_card pmpro_content_message\"><div class=\"pmpro_card_content\">Dieser Inhalt ist nur f\u00fcr Benutzer der Gruppe: Medizinische Fachperson zug\u00e4nglich <br \/><a href=\"https:\/\/medizinonline.com\/fr\/mon-compte\/paquets\/\">Jetzt beitreten<\/a><\/div><div class=\"pmpro_card_actions pmpro_font-medium\">Already a member? <a href=\"https:\/\/medizinonline.com\/fr\/se-connecter\/?redirect_to=https%3A%2F%2Fmedizinonline.com%2Ffr%2Flataxie-de-friedreich-quand-le-metabolisme-energetique-sattaque-au-systeme-nerveux%2F\">Connectez-vous ici<\/a><\/div><\/div><\/div>","protected":false},"excerpt":{"rendered":"<p>Un manque d&#8217;\u00e9nergie plut\u00f4t qu&#8217;un stress oxydatif pur : de nouvelles donn\u00e9es montrent que dans l&#8217;ataxie de Friedreich, ce sont surtout des troubles du m\u00e9tabolisme des acides gras et des&#8230;&hellip;... <\/p>\n<div class=\"pmpro\"><div class=\"pmpro_card pmpro_content_message\"><div class=\"pmpro_card_content\">Dieser Inhalt ist nur f\u00fcr Benutzer der Gruppe: Medizinische Fachperson zug\u00e4nglich <br \/><a href=\"https:\/\/medizinonline.com\/fr\/mon-compte\/paquets\/\">Jetzt beitreten<\/a><\/div><div class=\"pmpro_card_actions pmpro_font-medium\">Already a member? <a href=\"https:\/\/medizinonline.com\/fr\/se-connecter\/?redirect_to=https%3A%2F%2Fmedizinonline.com%2Ffr%2Flataxie-de-friedreich-quand-le-metabolisme-energetique-sattaque-au-systeme-nerveux%2F\">Connectez-vous ici<\/a><\/div><\/div><\/div>","protected":false},"author":7,"featured_media":550381,"comment_status":"closed","ping_status":"closed","sticky":false,"template":"","format":"standard","meta":{"_acf_changed":false,"pmpro_default_level":"","cat_1_feature_home_top":false,"cat_2_editor_pick":false,"csco_eyebrow_text":"Ataxies","footnotes":""},"category":[11527,11531,11417,11383,11549],"tags":[84958,88875,88876,88877,88873,88874],"powerkit_post_featured":[],"class_list":["post-550380","post","type-post","status-publish","format-standard","has-post-thumbnail","category-etudes","category-formation-continue","category-genetique","category-neurologie-fr","category-rx-fr","tag-ataxie-de-friedreich","tag-ataxie-de-friedreich-physiopathologie","tag-ataxies","tag-deficit-en-frataxine","tag-frda","tag-fxn","pmpro-level-required","pmpro-level-1","pmpro-no-access"],"acf":[],"publishpress_future_action":{"enabled":false,"date":"2026-05-09 02:01:25","action":"change-status","newStatus":"draft","terms":[],"taxonomy":"category","extraData":[]},"publishpress_future_workflow_manual_trigger":{"enabledWorkflows":[]},"wpml_current_locale":"fr_FR","wpml_translations":{"it_IT":{"locale":"it_IT","id":550377,"slug":"atassia-di-friedreich-quando-il-metabolismo-energetico-attacca-il-sistema-nervoso","post_title":"Atassia di Friedreich: quando il metabolismo energetico attacca il sistema nervoso","href":"https:\/\/medizinonline.com\/it\/atassia-di-friedreich-quando-il-metabolismo-energetico-attacca-il-sistema-nervoso\/"},"pt_PT":{"locale":"pt_PT","id":550374,"slug":"ataxia-de-friedreich-quando-o-metabolismo-energetico-ataca-o-sistema-nervoso","post_title":"Ataxia de Friedreich: quando o metabolismo energ\u00e9tico ataca o sistema nervoso","href":"https:\/\/medizinonline.com\/pt-pt\/ataxia-de-friedreich-quando-o-metabolismo-energetico-ataca-o-sistema-nervoso\/"},"es_ES":{"locale":"es_ES","id":550371,"slug":"ataxia-de-friedreich-cuando-el-metabolismo-energetico-ataca-al-sistema-nervioso","post_title":"Ataxia de Friedreich: cuando el metabolismo energ\u00e9tico ataca al sistema nervioso","href":"https:\/\/medizinonline.com\/es\/ataxia-de-friedreich-cuando-el-metabolismo-energetico-ataca-al-sistema-nervioso\/"}},"_links":{"self":[{"href":"https:\/\/medizinonline.com\/fr\/wp-json\/wp\/v2\/posts\/550380","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/medizinonline.com\/fr\/wp-json\/wp\/v2\/posts"}],"about":[{"href":"https:\/\/medizinonline.com\/fr\/wp-json\/wp\/v2\/types\/post"}],"author":[{"embeddable":true,"href":"https:\/\/medizinonline.com\/fr\/wp-json\/wp\/v2\/users\/7"}],"replies":[{"embeddable":true,"href":"https:\/\/medizinonline.com\/fr\/wp-json\/wp\/v2\/comments?post=550380"}],"version-history":[{"count":1,"href":"https:\/\/medizinonline.com\/fr\/wp-json\/wp\/v2\/posts\/550380\/revisions"}],"predecessor-version":[{"id":550382,"href":"https:\/\/medizinonline.com\/fr\/wp-json\/wp\/v2\/posts\/550380\/revisions\/550382"}],"wp:featuredmedia":[{"embeddable":true,"href":"https:\/\/medizinonline.com\/fr\/wp-json\/wp\/v2\/media\/550381"}],"wp:attachment":[{"href":"https:\/\/medizinonline.com\/fr\/wp-json\/wp\/v2\/media?parent=550380"}],"wp:term":[{"taxonomy":"category","embeddable":true,"href":"https:\/\/medizinonline.com\/fr\/wp-json\/wp\/v2\/category?post=550380"},{"taxonomy":"post_tag","embeddable":true,"href":"https:\/\/medizinonline.com\/fr\/wp-json\/wp\/v2\/tags?post=550380"},{"taxonomy":"powerkit_post_featured","embeddable":true,"href":"https:\/\/medizinonline.com\/fr\/wp-json\/wp\/v2\/powerkit_post_featured?post=550380"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}