{"id":557025,"date":"2026-05-31T12:30:00","date_gmt":"2026-05-31T10:30:00","guid":{"rendered":"https:\/\/medizinonline.com\/?p=557025"},"modified":"2026-05-31T12:32:07","modified_gmt":"2026-05-31T10:32:07","slug":"une-fillette-de-8-ans-atteinte-du-syndrome-de-paetau-alias-trisomie-13","status":"publish","type":"post","link":"https:\/\/medizinonline.com\/fr\/une-fillette-de-8-ans-atteinte-du-syndrome-de-paetau-alias-trisomie-13\/","title":{"rendered":"Une fillette de 8 ans atteinte du syndrome de P\u00e4tau, alias trisomie 13"},"content":{"rendered":"\n<p class=\"wp-block-paragraph\"><strong>La dur\u00e9e m\u00e9diane de survie des enfants n\u00e9s vivants atteints de trisomie 13 compl\u00e8te est de 7 \u00e0 10 jours sans intervention m\u00e9dicale. Plus de 90% des nouveau-n\u00e9s atteints meurent au cours de leur premi\u00e8re ann\u00e9e de vie. Les facteurs de risque de d\u00e9c\u00e8s pr\u00e9coce sont le sexe masculin, la naissance pr\u00e9matur\u00e9e et la pr\u00e9sence de malformations cardiaques cong\u00e9nitales. Les causes de d\u00e9c\u00e8s les plus fr\u00e9quentes sont l&#8217;insuffisance cardiaque et l&#8217;apn\u00e9e centrale. Les patients qui survivent \u00e0 la p\u00e9riode de la petite enfance pr\u00e9sentent g\u00e9n\u00e9ralement de graves retards de d\u00e9veloppement psychomoteur, des troubles de la croissance, des d\u00e9ficiences intellectuelles et des crises convulsives.    <\/strong><\/p>\n\n<div class=\"pmpro\"><div class=\"pmpro_card pmpro_content_message\"><div class=\"pmpro_card_content\">Dieser Inhalt ist nur f\u00fcr Benutzer der Gruppe: Medizinische Fachperson zug\u00e4nglich <br \/><a href=\"https:\/\/medizinonline.com\/fr\/mon-compte\/paquets\/\">Jetzt beitreten<\/a><\/div><div class=\"pmpro_card_actions pmpro_font-medium\">Already a member? <a href=\"https:\/\/medizinonline.com\/fr\/se-connecter\/?redirect_to=https%3A%2F%2Fmedizinonline.com%2Ffr%2Fune-fillette-de-8-ans-atteinte-du-syndrome-de-paetau-alias-trisomie-13%2F\">Connectez-vous ici<\/a><\/div><\/div><\/div>","protected":false},"excerpt":{"rendered":"<p>La dur\u00e9e m\u00e9diane de survie des enfants n\u00e9s vivants atteints de trisomie 13 compl\u00e8te est de 7 \u00e0 10 jours sans intervention m\u00e9dicale. Plus de 90% des nouveau-n\u00e9s atteints meurent&#8230;&hellip;... <\/p>\n<div class=\"pmpro\"><div class=\"pmpro_card pmpro_content_message\"><div class=\"pmpro_card_content\">Dieser Inhalt ist nur f\u00fcr Benutzer der Gruppe: Medizinische Fachperson zug\u00e4nglich <br \/><a href=\"https:\/\/medizinonline.com\/fr\/mon-compte\/paquets\/\">Jetzt beitreten<\/a><\/div><div class=\"pmpro_card_actions pmpro_font-medium\">Already a member? <a href=\"https:\/\/medizinonline.com\/fr\/se-connecter\/?redirect_to=https%3A%2F%2Fmedizinonline.com%2Ffr%2Fune-fillette-de-8-ans-atteinte-du-syndrome-de-paetau-alias-trisomie-13%2F\">Connectez-vous ici<\/a><\/div><\/div><\/div>","protected":false},"author":7,"featured_media":557026,"comment_status":"closed","ping_status":"closed","sticky":false,"template":"","format":"standard","meta":{"_acf_changed":false,"pmpro_default_level":"","cat_1_feature_home_top":false,"cat_2_editor_pick":false,"csco_eyebrow_text":"\u00c9tude de cas  ","footnotes":""},"category":[11549,11541,11399,11531,11417,11315,11458],"tags":[93939,93942,16386,22715,23873,93940,12158,49872,93938,93941,93935,93936,93937],"powerkit_post_featured":[],"class_list":["post-557025","post","type-post","status-publish","format-standard","has-post-thumbnail","category-rx-fr","category-cases-fr","category-chirurgie-fr","category-formation-continue","category-genetique","category-medecine-interne-generale","category-pediatrie","tag-apnee-centrale","tag-convulsions","tag-defauts-cardiaques","tag-etude-de-cas","tag-facteurs-de-risque","tag-handicaps-mentaux","tag-insuffisance-cardiaque-fr","tag-naissance-prematuree","tag-retards-de-developpement","tag-sexe-masculin","tag-syndrome-de-paetau","tag-trisomie-13","tag-troubles-de-la-croissance-2","pmpro-level-required","pmpro-level-1","pmpro-no-access"],"acf":[],"publishpress_future_action":{"enabled":false,"date":"2026-07-14 16:15:32","action":"change-status","newStatus":"draft","terms":[],"taxonomy":"category","extraData":[]},"publishpress_future_workflow_manual_trigger":{"enabledWorkflows":[]},"wpml_current_locale":"fr_FR","wpml_translations":{"it_IT":{"locale":"it_IT","id":557022,"slug":"bambina-di-8-anni-con-sindrome-di-paetau-alias-trisomia-13","post_title":"Bambina di 8 anni con sindrome di P\u00e4tau, alias trisomia 13","href":"https:\/\/medizinonline.com\/it\/bambina-di-8-anni-con-sindrome-di-paetau-alias-trisomia-13\/"},"pt_PT":{"locale":"pt_PT","id":557019,"slug":"menina-de-8-anos-com-sindrome-de-paetau-tambem-conhecida-como-trissomia-13","post_title":"Menina de 8 anos com s\u00edndrome de P\u00e4tau, tamb\u00e9m conhecida como trissomia 13","href":"https:\/\/medizinonline.com\/pt-pt\/menina-de-8-anos-com-sindrome-de-paetau-tambem-conhecida-como-trissomia-13\/"},"es_ES":{"locale":"es_ES","id":557016,"slug":"nina-de-8-anos-con-sindrome-de-paetau-alias-trisomia-13","post_title":"Ni\u00f1a de 8 a\u00f1os con s\u00edndrome de P\u00e4tau alias trisom\u00eda 13","href":"https:\/\/medizinonline.com\/es\/nina-de-8-anos-con-sindrome-de-paetau-alias-trisomia-13\/"}},"_links":{"self":[{"href":"https:\/\/medizinonline.com\/fr\/wp-json\/wp\/v2\/posts\/557025","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/medizinonline.com\/fr\/wp-json\/wp\/v2\/posts"}],"about":[{"href":"https:\/\/medizinonline.com\/fr\/wp-json\/wp\/v2\/types\/post"}],"author":[{"embeddable":true,"href":"https:\/\/medizinonline.com\/fr\/wp-json\/wp\/v2\/users\/7"}],"replies":[{"embeddable":true,"href":"https:\/\/medizinonline.com\/fr\/wp-json\/wp\/v2\/comments?post=557025"}],"version-history":[{"count":2,"href":"https:\/\/medizinonline.com\/fr\/wp-json\/wp\/v2\/posts\/557025\/revisions"}],"predecessor-version":[{"id":557658,"href":"https:\/\/medizinonline.com\/fr\/wp-json\/wp\/v2\/posts\/557025\/revisions\/557658"}],"wp:featuredmedia":[{"embeddable":true,"href":"https:\/\/medizinonline.com\/fr\/wp-json\/wp\/v2\/media\/557026"}],"wp:attachment":[{"href":"https:\/\/medizinonline.com\/fr\/wp-json\/wp\/v2\/media?parent=557025"}],"wp:term":[{"taxonomy":"category","embeddable":true,"href":"https:\/\/medizinonline.com\/fr\/wp-json\/wp\/v2\/category?post=557025"},{"taxonomy":"post_tag","embeddable":true,"href":"https:\/\/medizinonline.com\/fr\/wp-json\/wp\/v2\/tags?post=557025"},{"taxonomy":"powerkit_post_featured","embeddable":true,"href":"https:\/\/medizinonline.com\/fr\/wp-json\/wp\/v2\/powerkit_post_featured?post=557025"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}