{"id":563487,"date":"2026-09-02T00:30:00","date_gmt":"2026-09-01T22:30:00","guid":{"rendered":"https:\/\/medizinonline.com\/?p=563487"},"modified":"2026-08-28T17:26:38","modified_gmt":"2026-08-28T15:26:38","slug":"nouvelles-options-therapeutiques-pour-la-pn-de-type-attrv","status":"publish","type":"post","link":"https:\/\/medizinonline.com\/fr\/nouvelles-options-therapeutiques-pour-la-pn-de-type-attrv\/","title":{"rendered":"Nouvelles options th\u00e9rapeutiques pour la PN de type ATTRv"},"content":{"rendered":"\n<figure class=\"wp-block-table\"><table class=\"has-fixed-layout\"><tbody><tr><td><strong>L&#8217;amylose h\u00e9r\u00e9ditaire \u00e0 transthyr\u00e9tine associ\u00e9e \u00e0 une polyneuropathie (ATTRv-PN) est une polyneuropathie h\u00e9r\u00e9ditaire progressive apparaissant \u00e0 l&#8217;\u00e2ge adulte, qui s&#8217;accompagne souvent d&#8217;une atteinte cardiaque. Un syndrome du canal carpien ainsi qu\u2019une d\u00e9nervation sensorielle et sudomotrice de la peau peuvent pr\u00e9c\u00e9der les sympt\u00f4mes d\u2019une polyneuropathie marqu\u00e9e. Le traitement n\u00e9cessite une th\u00e9rapie modificatrice de la maladie adapt\u00e9e au ph\u00e9notype, une prise en charge symptomatique et un suivi multidisciplinaire.<\/strong><\/td><\/tr><\/tbody><\/table><\/figure>\n\n<div class=\"pmpro\"><div class=\"pmpro_card pmpro_content_message\"><div class=\"pmpro_card_content\">Dieser Inhalt ist nur f\u00fcr Benutzer der Gruppe: Medizinische Fachperson zug\u00e4nglich <br \/><a href=\"https:\/\/medizinonline.com\/fr\/mon-compte\/paquets\/\">Jetzt beitreten<\/a><\/div><div class=\"pmpro_card_actions pmpro_font-medium\">Already a member? <a href=\"https:\/\/medizinonline.com\/fr\/se-connecter\/?redirect_to=https%3A%2F%2Fmedizinonline.com%2Ffr%2Fnouvelles-options-therapeutiques-pour-la-pn-de-type-attrv%2F\">Connectez-vous ici<\/a><\/div><\/div><\/div>","protected":false},"excerpt":{"rendered":"<p>L&#8217;amylose h\u00e9r\u00e9ditaire \u00e0 transthyr\u00e9tine associ\u00e9e \u00e0 une polyneuropathie (ATTRv-PN) est une polyneuropathie h\u00e9r\u00e9ditaire progressive apparaissant \u00e0 l&#8217;\u00e2ge adulte, qui s&#8217;accompagne souvent d&#8217;une atteinte cardiaque. Un syndrome du canal carpien ainsi&#8230;&hellip;... <\/p>\n<div class=\"pmpro\"><div class=\"pmpro_card pmpro_content_message\"><div class=\"pmpro_card_content\">Dieser Inhalt ist nur f\u00fcr Benutzer der Gruppe: Medizinische Fachperson zug\u00e4nglich <br \/><a href=\"https:\/\/medizinonline.com\/fr\/mon-compte\/paquets\/\">Jetzt beitreten<\/a><\/div><div class=\"pmpro_card_actions pmpro_font-medium\">Already a member? <a href=\"https:\/\/medizinonline.com\/fr\/se-connecter\/?redirect_to=https%3A%2F%2Fmedizinonline.com%2Ffr%2Fnouvelles-options-therapeutiques-pour-la-pn-de-type-attrv%2F\">Connectez-vous ici<\/a><\/div><\/div><\/div>","protected":false},"author":7,"featured_media":563492,"comment_status":"closed","ping_status":"closed","sticky":false,"template":"","format":"standard","meta":{"_acf_changed":false,"pmpro_default_level":"","cat_1_feature_home_top":false,"cat_2_editor_pick":false,"csco_eyebrow_text":"Amylose h\u00e9r\u00e9ditaire \u00e0 transthyr\u00e9tine associ\u00e9e \u00e0 une polyneuropathie","footnotes":"","_members_access_role":[],"_members_access_error":""},"category":[11549,11378,11527,11531,11414,11315,11383,11464],"tags":[99895,99896,99894,99898,99897,20173,94136,12573],"powerkit_post_featured":[],"class_list":["post-563487","post","type-post","status-publish","format-standard","has-post-thumbnail","category-rx-fr","category-cardiologie","category-etudes","category-formation-continue","category-gastro-enterologie-et-hepatologie","category-medecine-interne-generale","category-neurologie-fr","category-pharmacologie-et-toxicologie","tag-amylose-hereditaire","tag-amylose-hereditaire-a-la-transthyretine-associee-a-une-polyneuropathie","tag-attrv-pn","tag-elimination-de-lamyloide","tag-gen-silencer","tag-neuropathie-fr","tag-stabilisateurs-ttr","tag-therapie-fr","pmpro-level-required","pmpro-level-1","pmpro-no-access"],"acf":[],"publishpress_future_action":{"enabled":false,"date":"2026-09-09 02:34:35","action":"change-status","newStatus":"draft","terms":[],"taxonomy":"category","extraData":[]},"publishpress_future_workflow_manual_trigger":{"enabledWorkflows":[]},"wpml_current_locale":"fr_FR","wpml_translations":{"it_IT":{"locale":"it_IT","id":563494,"slug":"nuove-opzioni-terapeutiche-per-la-pn-di-tipo-attrv","post_title":"Nuove opzioni terapeutiche per la PN di tipo ATTRv","href":"https:\/\/medizinonline.com\/it\/nuove-opzioni-terapeutiche-per-la-pn-di-tipo-attrv\/"},"pt_PT":{"locale":"pt_PT","id":563502,"slug":"novas-opcoes-terapeuticas-para-a-pn-do-tipo-attrv","post_title":"Novas op\u00e7\u00f5es terap\u00eauticas para a PN do tipo ATTRv","href":"https:\/\/medizinonline.com\/pt-pt\/novas-opcoes-terapeuticas-para-a-pn-do-tipo-attrv\/"},"es_ES":{"locale":"es_ES","id":563517,"slug":"nuevas-opciones-terapeuticas-para-la-pn-de-tipo-attrv","post_title":"Nuevas opciones terap\u00e9uticas para la PN de tipo ATTRv","href":"https:\/\/medizinonline.com\/es\/nuevas-opciones-terapeuticas-para-la-pn-de-tipo-attrv\/"}},"_links":{"self":[{"href":"https:\/\/medizinonline.com\/fr\/wp-json\/wp\/v2\/posts\/563487","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/medizinonline.com\/fr\/wp-json\/wp\/v2\/posts"}],"about":[{"href":"https:\/\/medizinonline.com\/fr\/wp-json\/wp\/v2\/types\/post"}],"author":[{"embeddable":true,"href":"https:\/\/medizinonline.com\/fr\/wp-json\/wp\/v2\/users\/7"}],"replies":[{"embeddable":true,"href":"https:\/\/medizinonline.com\/fr\/wp-json\/wp\/v2\/comments?post=563487"}],"version-history":[{"count":1,"href":"https:\/\/medizinonline.com\/fr\/wp-json\/wp\/v2\/posts\/563487\/revisions"}],"predecessor-version":[{"id":563493,"href":"https:\/\/medizinonline.com\/fr\/wp-json\/wp\/v2\/posts\/563487\/revisions\/563493"}],"wp:featuredmedia":[{"embeddable":true,"href":"https:\/\/medizinonline.com\/fr\/wp-json\/wp\/v2\/media\/563492"}],"wp:attachment":[{"href":"https:\/\/medizinonline.com\/fr\/wp-json\/wp\/v2\/media?parent=563487"}],"wp:term":[{"taxonomy":"category","embeddable":true,"href":"https:\/\/medizinonline.com\/fr\/wp-json\/wp\/v2\/category?post=563487"},{"taxonomy":"post_tag","embeddable":true,"href":"https:\/\/medizinonline.com\/fr\/wp-json\/wp\/v2\/tags?post=563487"},{"taxonomy":"powerkit_post_featured","embeddable":true,"href":"https:\/\/medizinonline.com\/fr\/wp-json\/wp\/v2\/powerkit_post_featured?post=563487"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}