{"id":563780,"date":"2026-09-07T00:30:00","date_gmt":"2026-09-06T22:30:00","guid":{"rendered":"https:\/\/medizinonline.com\/?p=563780"},"modified":"2026-09-07T07:48:13","modified_gmt":"2026-09-07T05:48:13","slug":"la-maladie-de-darier-egalement-appelee-keratose-folliculaire-mise-a-jour-2026","status":"publish","type":"post","link":"https:\/\/medizinonline.com\/fr\/la-maladie-de-darier-egalement-appelee-keratose-folliculaire-mise-a-jour-2026\/","title":{"rendered":"La maladie de Darier, \u00e9galement appel\u00e9e k\u00e9ratose folliculaire \u2013 Mise \u00e0 jour 2026"},"content":{"rendered":"\n<p class=\"wp-block-paragraph\"><strong>La maladie de Darier est due \u00e0 des variants pathog\u00e8nes du g\u00e8ne ATP2A2. Les progr\u00e8s r\u00e9alis\u00e9s dans la compr\u00e9hension de la physiopathologie ont ouvert la voie au d\u00e9veloppement d\u2019approches th\u00e9rapeutiques innovantes, mais des recherches suppl\u00e9mentaires sont n\u00e9cessaires pour optimiser les r\u00e9sultats pour les patients. Cela se refl\u00e8te \u00e9galement dans la cr\u00e9ation, en 2025, de <em>l\u2019International Task Force for Morbus Darier<\/em> (DD-ITF). Chez les patients atteints de formes s\u00e9v\u00e8res ou r\u00e9fractaires de la maladie, les r\u00e9tino\u00efdes oraux restent consid\u00e9r\u00e9s comme le traitement syst\u00e9mique de premi\u00e8re intention, mais on observe de plus en plus de cas cliniques faisant \u00e9tat d\u2019une utilisation r\u00e9ussie de traitements anti-inflammatoires immunomodulateurs (inhibiteurs de JAK, produits biologiques). Cela sugg\u00e8re que des processus inflammatoires complexes interviennent dans la pathogen\u00e8se de la maladie.<\/strong><\/p>\n\n<div class=\"pmpro\"><div class=\"pmpro_card pmpro_content_message\"><div class=\"pmpro_card_content\">Dieser Inhalt ist nur f\u00fcr Benutzer der Gruppe: Medizinische Fachperson zug\u00e4nglich <br \/><a href=\"https:\/\/medizinonline.com\/fr\/mon-compte\/paquets\/\">Jetzt beitreten<\/a><\/div><div class=\"pmpro_card_actions pmpro_font-medium\">Already a member? <a href=\"https:\/\/medizinonline.com\/fr\/se-connecter\/?redirect_to=https%3A%2F%2Fmedizinonline.com%2Ffr%2Fla-maladie-de-darier-egalement-appelee-keratose-folliculaire-mise-a-jour-2026%2F\">Connectez-vous ici<\/a><\/div><\/div><\/div>","protected":false},"excerpt":{"rendered":"<p>La maladie de Darier est due \u00e0 des variants pathog\u00e8nes du g\u00e8ne ATP2A2. Les progr\u00e8s r\u00e9alis\u00e9s dans la compr\u00e9hension de la physiopathologie ont ouvert la voie au d\u00e9veloppement d\u2019approches th\u00e9rapeutiques&#8230;&hellip;... <\/p>\n<div class=\"pmpro\"><div class=\"pmpro_card pmpro_content_message\"><div class=\"pmpro_card_content\">Dieser Inhalt ist nur f\u00fcr Benutzer der Gruppe: Medizinische Fachperson zug\u00e4nglich <br \/><a href=\"https:\/\/medizinonline.com\/fr\/mon-compte\/paquets\/\">Jetzt beitreten<\/a><\/div><div class=\"pmpro_card_actions pmpro_font-medium\">Already a member? <a href=\"https:\/\/medizinonline.com\/fr\/se-connecter\/?redirect_to=https%3A%2F%2Fmedizinonline.com%2Ffr%2Fla-maladie-de-darier-egalement-appelee-keratose-folliculaire-mise-a-jour-2026%2F\">Connectez-vous ici<\/a><\/div><\/div><\/div>","protected":false},"author":7,"featured_media":563785,"comment_status":"closed","ping_status":"closed","sticky":false,"template":"","format":"standard","meta":{"_acf_changed":false,"pmpro_default_level":"","cat_1_feature_home_top":false,"cat_2_editor_pick":false,"csco_eyebrow_text":"G\u00e9nodermatoses rares : du diagnostic au traitement","footnotes":"","_members_access_role":[],"_members_access_error":""},"category":[22616,11541,11362,11527,11464,11549],"tags":[99980,99982,14154,99979,29551,99981,65783,99978,41213,12408,31536,78054,99977],"powerkit_post_featured":[],"class_list":["post-563780","post","type-post","status-publish","format-standard","has-post-thumbnail","category-formation-continue-cme","category-cases-fr","category-dermatologie-et-venerologie","category-etudes","category-pharmacologie-et-toxicologie","category-rx-fr","tag-approches-therapeutiques-innovantes","tag-dd-itf","tag-diagnostic-fr","tag-gene-atp2a2","tag-genodermatoses-fr","tag-groupe-de-travail-international-sur-la-maladie-de-darier","tag-jak-i-fr","tag-keratose-folliculaire","tag-maladie-de-darier","tag-medicaments-biologiques","tag-pathogenese-fr","tag-retinoides-oraux","tag-therapies-immunomodulatrices","pmpro-level-required","pmpro-level-1","pmpro-no-access"],"acf":[],"publishpress_future_action":{"enabled":false,"date":"2026-09-14 09:32:38","action":"change-status","newStatus":"draft","terms":[],"taxonomy":"category","extraData":[]},"publishpress_future_workflow_manual_trigger":{"enabledWorkflows":[]},"wpml_current_locale":"fr_FR","wpml_translations":{"it_IT":{"locale":"it_IT","id":563790,"slug":"malattia-di-darier-nota-anche-come-cheratosi-follicolare-aggiornamento-2026","post_title":"Malattia di Darier, nota anche come cheratosi follicolare \u2013 Aggiornamento 2026","href":"https:\/\/medizinonline.com\/it\/malattia-di-darier-nota-anche-come-cheratosi-follicolare-aggiornamento-2026\/"},"pt_PT":{"locale":"pt_PT","id":563800,"slug":"doenca-de-darier-tambem-conhecida-como-queratose-folicular-atualizacao-de-2026","post_title":"Doen\u00e7a de Darier, tamb\u00e9m conhecida como queratose folicular \u2013 Atualiza\u00e7\u00e3o de 2026","href":"https:\/\/medizinonline.com\/pt-pt\/doenca-de-darier-tambem-conhecida-como-queratose-folicular-atualizacao-de-2026\/"},"es_ES":{"locale":"es_ES","id":563766,"slug":"enfermedad-de-darier-tambien-conocida-como-queratosis-folicular-actualizacion-de-2026","post_title":"Enfermedad de Darier, tambi\u00e9n conocida como queratosis folicular \u2013 Actualizaci\u00f3n de 2026","href":"https:\/\/medizinonline.com\/es\/enfermedad-de-darier-tambien-conocida-como-queratosis-folicular-actualizacion-de-2026\/"}},"_links":{"self":[{"href":"https:\/\/medizinonline.com\/fr\/wp-json\/wp\/v2\/posts\/563780","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/medizinonline.com\/fr\/wp-json\/wp\/v2\/posts"}],"about":[{"href":"https:\/\/medizinonline.com\/fr\/wp-json\/wp\/v2\/types\/post"}],"author":[{"embeddable":true,"href":"https:\/\/medizinonline.com\/fr\/wp-json\/wp\/v2\/users\/7"}],"replies":[{"embeddable":true,"href":"https:\/\/medizinonline.com\/fr\/wp-json\/wp\/v2\/comments?post=563780"}],"version-history":[{"count":1,"href":"https:\/\/medizinonline.com\/fr\/wp-json\/wp\/v2\/posts\/563780\/revisions"}],"predecessor-version":[{"id":564511,"href":"https:\/\/medizinonline.com\/fr\/wp-json\/wp\/v2\/posts\/563780\/revisions\/564511"}],"wp:featuredmedia":[{"embeddable":true,"href":"https:\/\/medizinonline.com\/fr\/wp-json\/wp\/v2\/media\/563785"}],"wp:attachment":[{"href":"https:\/\/medizinonline.com\/fr\/wp-json\/wp\/v2\/media?parent=563780"}],"wp:term":[{"taxonomy":"category","embeddable":true,"href":"https:\/\/medizinonline.com\/fr\/wp-json\/wp\/v2\/category?post=563780"},{"taxonomy":"post_tag","embeddable":true,"href":"https:\/\/medizinonline.com\/fr\/wp-json\/wp\/v2\/tags?post=563780"},{"taxonomy":"powerkit_post_featured","embeddable":true,"href":"https:\/\/medizinonline.com\/fr\/wp-json\/wp\/v2\/powerkit_post_featured?post=563780"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}