{"id":550377,"date":"2026-03-05T21:58:17","date_gmt":"2026-03-05T20:58:17","guid":{"rendered":"https:\/\/medizinonline.com\/?p=550377"},"modified":"2026-03-05T21:58:29","modified_gmt":"2026-03-05T20:58:29","slug":"atassia-di-friedreich-quando-il-metabolismo-energetico-attacca-il-sistema-nervoso","status":"publish","type":"post","link":"https:\/\/medizinonline.com\/it\/atassia-di-friedreich-quando-il-metabolismo-energetico-attacca-il-sistema-nervoso\/","title":{"rendered":"Atassia di Friedreich: quando il metabolismo energetico attacca il sistema nervoso"},"content":{"rendered":"\n<p class=\"wp-block-paragraph\"><strong>Carenza energetica invece di puro stress ossidativo: nuovi dati mostrano che nell&#8217;atassia di Friedreich, i disturbi del metabolismo degli acidi grassi e dei corpi chetonici in particolare contribuiscono alla neurodegenerazione selettiva. L&#8217;articolo illustra la fisiopatologia, spiega la vulnerabilit\u00e0 neuronale e mostra quali vie di segnalazione metabolica potrebbero essere affrontate terapeuticamente in futuro. <\/strong><\/p>\n\n<div class=\"pmpro\"><div class=\"pmpro_card pmpro_content_message\"><div class=\"pmpro_card_content\">Dieser Inhalt ist nur f\u00fcr Benutzer der Gruppe: Medizinische Fachperson zug\u00e4nglich <br \/><a href=\"https:\/\/medizinonline.com\/it\/il-mio-conto\/pacchetti\/\">Jetzt beitreten<\/a><\/div><div class=\"pmpro_card_actions pmpro_font-medium\">Already a member? <a href=\"https:\/\/medizinonline.com\/it\/effettuare-il-login\/?redirect_to=https%3A%2F%2Fmedizinonline.com%2Fit%2Fatassia-di-friedreich-quando-il-metabolismo-energetico-attacca-il-sistema-nervoso%2F\">Accedi<\/a><\/div><\/div><\/div>","protected":false},"excerpt":{"rendered":"<p>Carenza energetica invece di puro stress ossidativo: nuovi dati mostrano che nell&#8217;atassia di Friedreich, i disturbi del metabolismo degli acidi grassi e dei corpi chetonici in particolare contribuiscono alla neurodegenerazione&#8230;&hellip;... <\/p>\n<div class=\"pmpro\"><div class=\"pmpro_card pmpro_content_message\"><div class=\"pmpro_card_content\">Dieser Inhalt ist nur f\u00fcr Benutzer der Gruppe: Medizinische Fachperson zug\u00e4nglich <br \/><a href=\"https:\/\/medizinonline.com\/it\/il-mio-conto\/pacchetti\/\">Jetzt beitreten<\/a><\/div><div class=\"pmpro_card_actions pmpro_font-medium\">Already a member? <a href=\"https:\/\/medizinonline.com\/it\/effettuare-il-login\/?redirect_to=https%3A%2F%2Fmedizinonline.com%2Fit%2Fatassia-di-friedreich-quando-il-metabolismo-energetico-attacca-il-sistema-nervoso%2F\">Accedi<\/a><\/div><\/div><\/div>","protected":false},"author":7,"featured_media":550378,"comment_status":"closed","ping_status":"closed","sticky":false,"template":"","format":"standard","meta":{"_acf_changed":false,"pmpro_default_level":"","cat_1_feature_home_top":false,"cat_2_editor_pick":false,"csco_eyebrow_text":"Atassie","footnotes":""},"category":[11550,11519,11405,11371,11515],"tags":[84953,88871,88872,88870,88607,88869],"powerkit_post_featured":[],"class_list":["post-550377","post","type-post","status-publish","format-standard","has-post-thumbnail","category-rx-it","category-formazione-continua","category-genetica-it","category-neurologia-it","category-studi","tag-atassia-di-friedreich","tag-atassie","tag-carenza-di-frataxina","tag-fisiopatologia-dellatassia-di-friedreich","tag-frda","tag-fxn","pmpro-level-required","pmpro-level-1","pmpro-no-access"],"acf":[],"publishpress_future_action":{"enabled":false,"date":"2026-07-13 09:45:56","action":"change-status","newStatus":"draft","terms":[],"taxonomy":"category","extraData":[]},"publishpress_future_workflow_manual_trigger":{"enabledWorkflows":[]},"wpml_current_locale":"it_IT","wpml_translations":{"pt_PT":{"locale":"pt_PT","id":550374,"slug":"ataxia-de-friedreich-quando-o-metabolismo-energetico-ataca-o-sistema-nervoso","post_title":"Ataxia de Friedreich: quando o metabolismo energ\u00e9tico ataca o sistema nervoso","href":"https:\/\/medizinonline.com\/pt-pt\/ataxia-de-friedreich-quando-o-metabolismo-energetico-ataca-o-sistema-nervoso\/"},"es_ES":{"locale":"es_ES","id":550371,"slug":"ataxia-de-friedreich-cuando-el-metabolismo-energetico-ataca-al-sistema-nervioso","post_title":"Ataxia de Friedreich: cuando el metabolismo energ\u00e9tico ataca al sistema nervioso","href":"https:\/\/medizinonline.com\/es\/ataxia-de-friedreich-cuando-el-metabolismo-energetico-ataca-al-sistema-nervioso\/"}},"_links":{"self":[{"href":"https:\/\/medizinonline.com\/it\/wp-json\/wp\/v2\/posts\/550377","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/medizinonline.com\/it\/wp-json\/wp\/v2\/posts"}],"about":[{"href":"https:\/\/medizinonline.com\/it\/wp-json\/wp\/v2\/types\/post"}],"author":[{"embeddable":true,"href":"https:\/\/medizinonline.com\/it\/wp-json\/wp\/v2\/users\/7"}],"replies":[{"embeddable":true,"href":"https:\/\/medizinonline.com\/it\/wp-json\/wp\/v2\/comments?post=550377"}],"version-history":[{"count":1,"href":"https:\/\/medizinonline.com\/it\/wp-json\/wp\/v2\/posts\/550377\/revisions"}],"predecessor-version":[{"id":550379,"href":"https:\/\/medizinonline.com\/it\/wp-json\/wp\/v2\/posts\/550377\/revisions\/550379"}],"wp:featuredmedia":[{"embeddable":true,"href":"https:\/\/medizinonline.com\/it\/wp-json\/wp\/v2\/media\/550378"}],"wp:attachment":[{"href":"https:\/\/medizinonline.com\/it\/wp-json\/wp\/v2\/media?parent=550377"}],"wp:term":[{"taxonomy":"category","embeddable":true,"href":"https:\/\/medizinonline.com\/it\/wp-json\/wp\/v2\/category?post=550377"},{"taxonomy":"post_tag","embeddable":true,"href":"https:\/\/medizinonline.com\/it\/wp-json\/wp\/v2\/tags?post=550377"},{"taxonomy":"powerkit_post_featured","embeddable":true,"href":"https:\/\/medizinonline.com\/it\/wp-json\/wp\/v2\/powerkit_post_featured?post=550377"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}