{"id":393535,"date":"2025-02-13T00:01:00","date_gmt":"2025-02-12T23:01:00","guid":{"rendered":"https:\/\/medizinonline.com\/?p=393535"},"modified":"2025-02-12T22:10:51","modified_gmt":"2025-02-12T21:10:51","slug":"sindrome-de-wolfram","status":"publish","type":"post","link":"https:\/\/medizinonline.com\/pt-pt\/sindrome-de-wolfram\/","title":{"rendered":"S\u00edndrome de Wolfram"},"content":{"rendered":"\n<p><strong>O termo s\u00edndrome &#8220;DIDMOAD&#8221; &#8211; um acr\u00f3nimo para os sintomas carater\u00edsticos &#8211; serve como nome alternativo para esta doen\u00e7a neurodegenerativa autoss\u00f3mica recessiva, que foi descrita pela primeira vez em 1938: Diabetes Insipidus, Diabetes Mellitus, Atrofia \u00d3tica e Surdez\/Surdez. Na maioria dos doentes, podem ser detectadas muta\u00e7\u00f5es no gene WFS1. <\/strong><\/p>\n\n\n\n<div class=\"pmpro\"><div class=\"pmpro_card pmpro_content_message\"><div class=\"pmpro_card_content\">Dieser Inhalt ist nur f\u00fcr Benutzer der Gruppe: Medizinische Fachperson zug\u00e4nglich <br \/><a href=\"https:\/\/medizinonline.com\/pt-pt\/a-minha-conta\/pacotes\/\">Jetzt beitreten<\/a><\/div><div class=\"pmpro_card_actions pmpro_font-medium\">Already a member? <a href=\"https:\/\/medizinonline.com\/pt-pt\/iniciar-sessao\/?redirect_to=https%3A%2F%2Fmedizinonline.com%2Fpt-pt%2Fsindrome-de-wolfram%2F\">Log in here<\/a><\/div><\/div><\/div>","protected":false},"excerpt":{"rendered":"<p>O termo s\u00edndrome &#8220;DIDMOAD&#8221; &#8211; um acr\u00f3nimo para os sintomas carater\u00edsticos &#8211; serve como nome alternativo para esta doen\u00e7a neurodegenerativa autoss\u00f3mica recessiva, que foi descrita pela primeira vez em 1938:&#8230;&hellip;... <\/p>\n<div class=\"pmpro\"><div class=\"pmpro_card pmpro_content_message\"><div class=\"pmpro_card_content\">Dieser Inhalt ist nur f\u00fcr Benutzer der Gruppe: Medizinische Fachperson zug\u00e4nglich <br \/><a href=\"https:\/\/medizinonline.com\/pt-pt\/a-minha-conta\/pacotes\/\">Jetzt beitreten<\/a><\/div><div class=\"pmpro_card_actions pmpro_font-medium\">Already a member? <a href=\"https:\/\/medizinonline.com\/pt-pt\/iniciar-sessao\/?redirect_to=https%3A%2F%2Fmedizinonline.com%2Fpt-pt%2Fsindrome-de-wolfram%2F\">Log in here<\/a><\/div><\/div><\/div>","protected":false},"author":7,"featured_media":393541,"comment_status":"closed","ping_status":"closed","sticky":false,"template":"","format":"standard","meta":{"_acf_changed":false,"pmpro_default_level":"","cat_1_feature_home_top":false,"cat_2_editor_pick":false,"csco_eyebrow_text":"Doen\u00e7as raras","footnotes":""},"category":[11551,11367,11397,11521,11524,11411,11305,11426,11374,11439,11481,11507],"tags":[11677,80736,26266,13067,80737,80739],"powerkit_post_featured":[],"class_list":["post-393535","post","type-post","status-publish","format-standard","has-post-thumbnail","category-rx-pt","category-cardiologia-pt-pt","category-endocrinologia-e-diabetologia-2","category-estudos","category-formacao-continua","category-genetica-pt-pt","category-medicina-interna-geral","category-nefrologia-pt-pt","category-neurologia-pt-pt","category-orl-pt-pt","category-psiquiatria-e-psicoterapia","category-urologia-pt-pt","tag-diabetes-pt-pt","tag-didmoad-pt-pt","tag-doencas-raras-pt-pt","tag-mutacoes","tag-sindrome-de-wolfram-pt-pt","tag-wfs1-pt-pt","pmpro-level-required","pmpro-level-1","pmpro-no-access"],"acf":[],"publishpress_future_action":{"enabled":false,"date":"2026-04-13 16:52:25","action":"change-status","newStatus":"draft","terms":[],"taxonomy":"category","extraData":[]},"publishpress_future_workflow_manual_trigger":{"enabledWorkflows":[]},"wpml_current_locale":"pt_PT","wpml_translations":{"es_ES":{"locale":"es_ES","id":393528,"slug":"sindrome-de-wolfram","post_title":"S\u00edndrome de Wolfram","href":"https:\/\/medizinonline.com\/es\/sindrome-de-wolfram\/"}},"_links":{"self":[{"href":"https:\/\/medizinonline.com\/pt-pt\/wp-json\/wp\/v2\/posts\/393535","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/medizinonline.com\/pt-pt\/wp-json\/wp\/v2\/posts"}],"about":[{"href":"https:\/\/medizinonline.com\/pt-pt\/wp-json\/wp\/v2\/types\/post"}],"author":[{"embeddable":true,"href":"https:\/\/medizinonline.com\/pt-pt\/wp-json\/wp\/v2\/users\/7"}],"replies":[{"embeddable":true,"href":"https:\/\/medizinonline.com\/pt-pt\/wp-json\/wp\/v2\/comments?post=393535"}],"version-history":[{"count":3,"href":"https:\/\/medizinonline.com\/pt-pt\/wp-json\/wp\/v2\/posts\/393535\/revisions"}],"predecessor-version":[{"id":394894,"href":"https:\/\/medizinonline.com\/pt-pt\/wp-json\/wp\/v2\/posts\/393535\/revisions\/394894"}],"wp:featuredmedia":[{"embeddable":true,"href":"https:\/\/medizinonline.com\/pt-pt\/wp-json\/wp\/v2\/media\/393541"}],"wp:attachment":[{"href":"https:\/\/medizinonline.com\/pt-pt\/wp-json\/wp\/v2\/media?parent=393535"}],"wp:term":[{"taxonomy":"category","embeddable":true,"href":"https:\/\/medizinonline.com\/pt-pt\/wp-json\/wp\/v2\/category?post=393535"},{"taxonomy":"post_tag","embeddable":true,"href":"https:\/\/medizinonline.com\/pt-pt\/wp-json\/wp\/v2\/tags?post=393535"},{"taxonomy":"powerkit_post_featured","embeddable":true,"href":"https:\/\/medizinonline.com\/pt-pt\/wp-json\/wp\/v2\/powerkit_post_featured?post=393535"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}