{"id":550374,"date":"2026-03-05T21:58:17","date_gmt":"2026-03-05T20:58:17","guid":{"rendered":"https:\/\/medizinonline.com\/?p=550374"},"modified":"2026-03-05T21:58:30","modified_gmt":"2026-03-05T20:58:30","slug":"ataxia-de-friedreich-quando-o-metabolismo-energetico-ataca-o-sistema-nervoso","status":"publish","type":"post","link":"https:\/\/medizinonline.com\/pt-pt\/ataxia-de-friedreich-quando-o-metabolismo-energetico-ataca-o-sistema-nervoso\/","title":{"rendered":"Ataxia de Friedreich: quando o metabolismo energ\u00e9tico ataca o sistema nervoso"},"content":{"rendered":"\n<p><strong>Defici\u00eancia energ\u00e9tica em vez de stress oxidativo puro: novos dados mostram que, na ataxia de Friedreich, as perturba\u00e7\u00f5es no metabolismo dos \u00e1cidos gordos e dos corpos cet\u00f3nicos, em particular, contribuem para a neurodegenera\u00e7\u00e3o selectiva. O artigo explica a fisiopatologia, explica a vulnerabilidade neuronal e mostra quais as vias de sinaliza\u00e7\u00e3o metab\u00f3lica que poder\u00e3o ser abordadas terapeuticamente no futuro. <\/strong><\/p>\n\n<div class=\"pmpro\"><div class=\"pmpro_card pmpro_content_message\"><div class=\"pmpro_card_content\">Dieser Inhalt ist nur f\u00fcr Benutzer der Gruppe: Medizinische Fachperson zug\u00e4nglich <br \/><a href=\"https:\/\/medizinonline.com\/pt-pt\/a-minha-conta\/pacotes\/\">Jetzt beitreten<\/a><\/div><div class=\"pmpro_card_actions pmpro_font-medium\">Already a member? <a href=\"https:\/\/medizinonline.com\/pt-pt\/iniciar-sessao\/?redirect_to=https%3A%2F%2Fmedizinonline.com%2Fpt-pt%2Fataxia-de-friedreich-quando-o-metabolismo-energetico-ataca-o-sistema-nervoso%2F\">Log in here<\/a><\/div><\/div><\/div>","protected":false},"excerpt":{"rendered":"<p>Defici\u00eancia energ\u00e9tica em vez de stress oxidativo puro: novos dados mostram que, na ataxia de Friedreich, as perturba\u00e7\u00f5es no metabolismo dos \u00e1cidos gordos e dos corpos cet\u00f3nicos, em particular, contribuem&#8230;&hellip;... <\/p>\n<div class=\"pmpro\"><div class=\"pmpro_card pmpro_content_message\"><div class=\"pmpro_card_content\">Dieser Inhalt ist nur f\u00fcr Benutzer der Gruppe: Medizinische Fachperson zug\u00e4nglich <br \/><a href=\"https:\/\/medizinonline.com\/pt-pt\/a-minha-conta\/pacotes\/\">Jetzt beitreten<\/a><\/div><div class=\"pmpro_card_actions pmpro_font-medium\">Already a member? <a href=\"https:\/\/medizinonline.com\/pt-pt\/iniciar-sessao\/?redirect_to=https%3A%2F%2Fmedizinonline.com%2Fpt-pt%2Fataxia-de-friedreich-quando-o-metabolismo-energetico-ataca-o-sistema-nervoso%2F\">Log in here<\/a><\/div><\/div><\/div>","protected":false},"author":7,"featured_media":550375,"comment_status":"closed","ping_status":"closed","sticky":false,"template":"","format":"standard","meta":{"_acf_changed":false,"pmpro_default_level":"","cat_1_feature_home_top":false,"cat_2_editor_pick":false,"csco_eyebrow_text":"Ataxias","footnotes":""},"category":[11521,11524,11411,11374,11551],"tags":[84949,88866,88867,88865,88863,88864],"powerkit_post_featured":[],"class_list":["post-550374","post","type-post","status-publish","format-standard","has-post-thumbnail","category-estudos","category-formacao-continua","category-genetica-pt-pt","category-neurologia-pt-pt","category-rx-pt","tag-ataxia-de-friedreich-pt-pt","tag-ataxias","tag-deficiencia-de-frataxina","tag-fisiopatologia-da-ataxia-de-friedreich","tag-frda","tag-fxn","pmpro-level-required","pmpro-level-1","pmpro-no-access"],"acf":[],"publishpress_future_action":{"enabled":false,"date":"2026-04-28 21:53:16","action":"change-status","newStatus":"draft","terms":[],"taxonomy":"category","extraData":[]},"publishpress_future_workflow_manual_trigger":{"enabledWorkflows":[]},"wpml_current_locale":"pt_PT","wpml_translations":{"es_ES":{"locale":"es_ES","id":550371,"slug":"ataxia-de-friedreich-cuando-el-metabolismo-energetico-ataca-al-sistema-nervioso","post_title":"Ataxia de Friedreich: cuando el metabolismo energ\u00e9tico ataca al sistema nervioso","href":"https:\/\/medizinonline.com\/es\/ataxia-de-friedreich-cuando-el-metabolismo-energetico-ataca-al-sistema-nervioso\/"}},"_links":{"self":[{"href":"https:\/\/medizinonline.com\/pt-pt\/wp-json\/wp\/v2\/posts\/550374","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/medizinonline.com\/pt-pt\/wp-json\/wp\/v2\/posts"}],"about":[{"href":"https:\/\/medizinonline.com\/pt-pt\/wp-json\/wp\/v2\/types\/post"}],"author":[{"embeddable":true,"href":"https:\/\/medizinonline.com\/pt-pt\/wp-json\/wp\/v2\/users\/7"}],"replies":[{"embeddable":true,"href":"https:\/\/medizinonline.com\/pt-pt\/wp-json\/wp\/v2\/comments?post=550374"}],"version-history":[{"count":1,"href":"https:\/\/medizinonline.com\/pt-pt\/wp-json\/wp\/v2\/posts\/550374\/revisions"}],"predecessor-version":[{"id":550376,"href":"https:\/\/medizinonline.com\/pt-pt\/wp-json\/wp\/v2\/posts\/550374\/revisions\/550376"}],"wp:featuredmedia":[{"embeddable":true,"href":"https:\/\/medizinonline.com\/pt-pt\/wp-json\/wp\/v2\/media\/550375"}],"wp:attachment":[{"href":"https:\/\/medizinonline.com\/pt-pt\/wp-json\/wp\/v2\/media?parent=550374"}],"wp:term":[{"taxonomy":"category","embeddable":true,"href":"https:\/\/medizinonline.com\/pt-pt\/wp-json\/wp\/v2\/category?post=550374"},{"taxonomy":"post_tag","embeddable":true,"href":"https:\/\/medizinonline.com\/pt-pt\/wp-json\/wp\/v2\/tags?post=550374"},{"taxonomy":"powerkit_post_featured","embeddable":true,"href":"https:\/\/medizinonline.com\/pt-pt\/wp-json\/wp\/v2\/powerkit_post_featured?post=550374"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}