Primary cutaneous lymphomas are a heterogeneous group of lymphoproliferative T-cell or B-cell neoplasms. Skin lymphomas are among the rare forms of skin cancer. Clinical inspection has an important role in establishing the diagnosis. Often, the suspected diagnosis is confirmed in the subsequent histological and immunohistochemical examinations. The treatment options depend, among other things, on the stage of the tumor disease. Especially in the field of cutaneous T-cell lymphomas, interesting new therapeutic strategies have been developed.