Update on Idiopathic Pulmonary Fibrosis

Interstitial lung diseases (ILDs) encompass more than 100 conditions. They represent a heterogeneous group of acute or chronic lung diseases that are characterized—to varying degrees—by inflammation and uncontrolled connective tissue formation, leading to scarring and stiffening of the lungs. The initial presentation of IPF is insidious dyspnea on exertion and a dry cough; the prognosis is poor.