KID syndrome – a rare ectodermal dysplasia

Keratitis-ichthyosis-deafness syndrome (KID) is a very rare genodermatosis. The main symptoms include ichthyosiform scaling of the skin, hyperkeratosis of the palms, sensory deafness and keratitis. Typical complications are severe skin infections and development of cutaneous neoplasms. There is currently no approved causal therapy for KID syndrome. In individual cases, the use of acitretin has proved helpful – as in the case of a patient who was treated at the Dermatology Clinic of the University Hospital Erlangen (Germany).